A number of drugs and toxins are associated with the development of PAH. The association between exposure to drugs and toxins and PAH is classified as definite or possible, as proposed at the 6th WSPH.

Definite associationPossible association
Aminorex
Benfluorex
Dasatinib
Dexfenfluramine Fenfluramine
Methamphetamines
Toxic rapeseed oil
Alkylating agents (cyclophosphamide, mitomycin C)
Amphetamines
Bosutinib
Cocaine
Diazoxide
Direct-acting antiviral agents against hepatitis C virus (sofosbuvir)
Indirubin (Chinese herb Qing-Dai)
Interferon alpha and beta
Leflunomide
L-tryptophan
Phenylpropanolamine
Ponatinib
Selective proteasome inhibitors (carfilzomib)
Solvents (trichloroethylene)
St John’s Wort